Journal of Oral Health and Community Dentistry

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VOLUME 8 , ISSUE 1 ( January-April, 2014 ) > List of Articles

CASE REPORT

Oral and Dental Findings of the Longest Surviving Patient with Hoyeraal-Hreidarsson Syndrome

AE Sekerci, Y Sisman, A Keskinrüzgar, E Unal, M Karakukcu, MA Ozdemir

Citation Information : Sekerci A, Sisman Y, Keskinrüzgar A, Unal E, Karakukcu M, Ozdemir M. Oral and Dental Findings of the Longest Surviving Patient with Hoyeraal-Hreidarsson Syndrome. J Oral Health Comm Dent 2014; 8 (1):65-69.

DOI: 10.5005/johcd-8-1-65

License: CC BY-NC 3.0

Published Online: 00-01-2014

Copyright Statement:  Copyright © 2014; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Hoyeraal-Hreidarsson syndrome (HHS) is a severe multisystem disorder associated with premature mortality, due to bone marrow failure. Because HHS is a very rare disease and almost all cases die before 7 years of age, the dental development and dental findings of HHS patients are still not clear. According to our knowledge only twenty seven cases were reported up to now and we did not find any report focusing on the dental evaluation of HHS patients. Therefore, in this report, we aimed to present the dental findings of a twenty-year old patient with HHS.


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